Home Learn About IPF Understanding IPF

Although idiopathic pulmonary fibrosis (IPF) can be a complicated disease, we'll help you understand what it is, how it affects the body, and why treating IPF is important.

The more you know, the more empowered you and your loved ones will be to make important decisions about your care. Scroll down to learn more.

Quick Fact: IPF affects up to 132,000 people in the U.S.


IPF is a rare, serious, and progressive disease that gets worse over time and causes permanent scarring of the lungs, which results in impaired lung function. It’s also unpredictable—no one knows who will get IPF or how quickly it will progress.

Idiopathic Definition

Idiopathic means the cause of the disease is unknown

Pulmonary Definition

Pulmonary means it impacts the lungs

Fibrosis Definition

Fibrosis means scarring

Find additional information about IPF and how OFEV® (nintedanib) can help.

download this helpful brochure


Diagnosing IPF isn’t always easy. That’s because IPF is deceptive—its symptoms can resemble more common conditions, making it easy to confuse IPF with other diseases, including COPD, asthma, and congestive heart failure.

An accurate diagnosis is important. The sooner an accurate diagnosis can be made, the sooner treatment options can be discussed.

Since IPF is a progressive disease that gets worse over time, starting treatment is important to slow disease progression.

Want to learn more about how IPF progresses and why starting treatment is important?


“Please, if you’ve been diagnosed, get educated about this disease. Know your options. Try and slow the progression with treatment.”

James, OFEV Mentor, Diagnosed with IPF in 2016

James, OFEV Mentor, Diagnosed with IPF in 2016

James, OFEV Mentor, Diagnosed with IPF in 2016